Refractory nonconvulsive status epilepticus in Creutzfeldt‐Jakob disease
- 1 September 2010
- journal article
- case report
- Published by Wiley in Epileptic Disorders
- Vol. 12 (3), 239-242
- https://doi.org/10.1684/epd.2010.0318
Abstract
Creutzfeldt-Jakob disease (CJD) is a rare human transmissible spongiform subacute encephalopathy. The most common clinical manifestations of CJD include rapidly progressive dementia, behavioural changes, cerebellar dysfunction and myoclonus. Other seizure types are rare and nonconvulsive status epilepticus (SE) is exceptional. We report a case of a 44-year-old man who presented a psychotic episode followed by akinetic mutism and refractory nonconvulsive SE. The final diagnosis was CJD. Continuous video-EEG monitoring revealed the ictal pattern of nonconvulsive SE to be periodic sharp wave complexes characteristic of CJD. [Published with video sequences].Keywords
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