Atypical Thymic Carcinoid and Malignant Somatostatinoma in Type I Multiple Endocrine Neoplasia Syndrome
- 1 June 2003
- journal article
- case report
- Published by Ovid Technologies (Wolters Kluwer Health) in American Journal of Clinical Oncology
- Vol. 26 (3), 270-272
- https://doi.org/10.1097/01.coc.0000020584.56294.72
Abstract
Thymic carcinoid and malignant somatostatinoma are both rare, and their concurrent presence in multiple endocrine neoplasia type 1 (MEN-1) has never been reported in the English literature to date. We present a patient with thymic carcinoid and malignant somatostatinoma in association with MEN-1. The patient eventually died of pulmonary aspergillosis and respiratory failure. Autopsy showed a 16 x 10 x 8-cm thymic carcinoid tumor, parathyroid and adrenal gland hyperplasia, and malignant somatostatinoma of the pancreas with a metastatic tumor over the splenic hilum.Keywords
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