Cole, Rauschkolb, and Toomey in January, 1930, reported a case of "Dyskeratosis Congenita with Pigmentation, Dystrophia Unguis, and Leukokeratosis Oris."1 They added to their case, two cases (brothers) of M. F. Engman Sr., who were presented before the Chicago Dermatological Society at the Nov. 25, 1925, meeting as "A Unique Case of Reticular Pigmentation of the Skin with Atrophy."2 These two brothers, the cases of M. F. Engman Sr., were reported by M. F. Engman Jr. in 1935 as "Congenital Atrophy of the Skin with Reticular Pigmentation."3 Garb and Rubin reported the cases of two brothers in 1944, previously presented by Wise before the New York Dermatological Society, with improvement in the leucoplakic patches in one of them, with androgenic medication.* Jansen reported the only European case from The Netherlands in 1951, under the title of "The So-Called `Dyskeratosis Congenita,'" with a subtitle "Pigmentatio