Parenteral nutrition in propionic and methylmalonic acidemia
- 1 August 1989
- journal article
- research article
- Published by Elsevier in The Journal of Pediatrics
- Vol. 115 (2), 235-241
- https://doi.org/10.1016/s0022-3476(89)80071-x
Abstract
No abstract availableThis publication has 12 references indexed in Scilit:
- Endogenous catabolism is the major source of toxic metabolites in isovaleric acidemiaThe Journal of Pediatrics, 1987
- Anorexia and altered serotonin metabolism in a patient with argininosuccinic aciduriaThe Journal of Pediatrics, 1986
- An evaluation of protein requirements in methylmalonic acidaemiaJournal of Inherited Metabolic Disease, 1984
- L-carnitine enhances excretion of propionyl coenzyme A as propionylcarnitine in propionic acidemia.Journal of Clinical Investigation, 1984
- Application of high resolution fast atom bombardment and constant B/E ratio linked scanning to the identification and analysis of acylcarnitines in metabolic diseaseJournal of Mass Spectrometry, 1984
- Dietary therapy in a girl with propionic acidemia: Supplement with leucine resulted in catch up growth.The Tohoku Journal of Experimental Medicine, 1983
- Total parenteral nutrition therapy of toxic maple syrup urine diseaseThe American Journal of Clinical Nutrition, 1982
- Propionic acidemia: A clinical updateThe Journal of Pediatrics, 1981
- Protein and essential amino acid requirements in a child with propionic acidemiaJournal of the American Dietetic Association, 1981
- A modified technique for the quantitative analysis of amino acids by gas chromatography using heptafluorobutyric n-propyl derivativesAnalytical Biochemistry, 1975