Chemotherapy and interferon‐α treatment of Erdheim–chester disease
- 25 August 2010
- journal article
- case report
- Published by Wiley in Pediatric Blood & Cancer
- Vol. 55 (4), 745-747
- https://doi.org/10.1002/pbc.22636
Abstract
Erdheim–Chester disease (ECD) is a rare non‐Langerhans cell histiocytosis of an unknown origin. The prognosis of ECD is variable, and it mainly depends on the involved anatomic sites. The treatment modalities have not been standardized. Interferon‐α (IFN) has been reported to be effective in the management of ECD. We report here on an uncommon case with ECD in a 17‐year‐old female who had multiple lesions in the whole body and she was treated with chemotherapy and IFN. She has remained disease‐free for 2 years after the completion of treatment. Pediatr Blood Cancer. 2010;55:745–747.Keywords
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