An unusual family of benign "X" linked muscular dystrophy with cardiac involvement.

Abstract
A family of benign X-linked muscular dystrophy is described. Two of the 3 affected members appear quite representative of Becker''s dystrophy. A 3rd shows no pseudohypertrophy, only gross atrophy, affecting proximal and distal muscles and also shows early onset contractures and ECG abnormalities. Two of the cases have distinctly abnormal ECG with extensive and deep Q waves and abnormal R/S ratios in VI. Both these have shown progression ECG abnormalities during a 2-yr follow-up.