Although primary involvement of the ocular muscles was recognized as a distinct entity many years ago by Gowers,1 other observers have followed Moebius'2 claim that the resulting weakness was due to nuclear degeneration. In 1951, however, Kiloh and Niven3 extensively reviewed the pertinent literature, presented five cases, and concluded that these entities were similar in their pathology, namely, primary disease of the ocular muscles. These observations have since been confirmed by biopsy of involved muscle4,5 and from autopsy material.6,7 The term ocular myopathy is now, therefore, in general usage for such cases. In this study, the clinical, and in particular the electromyographic, findings are presented in six patients with the diagnosis of ocular myopathy. I. Clinical Findings Report of Cases Case 1. —Ten years ago, this 54-year-old patient first noticed drooping of the right lid and double vision. Examination revealed complete right ptosis, without compensatory