A study of the low β-galactosidase activity in cystinotic fibroblasts: effects of cysteamine
- 21 January 1985
- journal article
- research article
- Published by Elsevier in Clinica Chimica Acta; International Journal of Clinical Chemistry
- Vol. 145 (1), 9-16
- https://doi.org/10.1016/0009-8981(85)90014-2
Abstract
No abstract availableKeywords
This publication has 11 references indexed in Scilit:
- The inhibition of β-galactosidase (Escherichia coli) by amino sugars and amino alcoholsCanadian Journal of Biochemistry, 1982
- Enhanced proteolytic degradation of normal β-galactosidase in the lysosomal storage disease with combined β-galactosidase and neuraminidase deficiencyBiochimica et Biophysica Acta (BBA) - Protein Structure and Molecular Enzymology, 1982
- Adverse Reactions to Oral Cysteamine Use in Nephropathie CystinosisDevelopmental Pharmacology and Therapeutics, 1981
- β-Galactosidase-Neuraminidase Deficiency: Restoration of β-Galactosidase Activity by Protease Inhibitors1The Journal of Biochemistry, 1981
- Recognition of abnormal lysosomal enzyme patterns in childhood leukaemia by isoelectric focusing, with special reference to some properties of abnormally expressed componentsLeukemia Research, 1981
- Activities of acid hydrolases in fibroblasts from normal and cystinotic childrenClinica Chimica Acta; International Journal of Clinical Chemistry, 1977
- In situ detection of mycoplasma contamination in cell cultures by fluorescent Hoechst 33258 stainExperimental Cell Research, 1977
- Cystinosis. Intracellular cystine depletion by aminothiols in vitro and in vivo.JCI Insight, 1976
- G1 Ganglioside β-Galactosidase APublished by Elsevier ,1974
- The assay of arylsulphatases A and B in human urineClinica Chimica Acta; International Journal of Clinical Chemistry, 1959