Analysis of the Hb M Milwaukee mutation at the DNA level

Abstract
Restriction endonuclease mapping of cellular DNA with the enzyme Sst I was used to detect the Hb Milwaukee mutation directly. Instead of a normal 15.5 kilobase pairs (kb) fragment which contains the normal .beta.-globin structural genes, in heterozygous Hb M Milwaukee DNA 2 additional fragments of 9.0 kb and 6.5 kb were obtained that are diagnostic for this anomaly. The position of Sst I sites within the .beta.-globin gene region could be established.