Abstract
A case of tuberous sclerosis occurring in a young man with mental deficiency, typical rash, and cardiac arrhythmia was described. The presentation with an arrhythmia is extremely rare having been reported only once before. Although the relation between rhabdomyomata and tuberous sclerosis is not clear, over 50% of rhabdomyomata occur in patients with overt tuberous sclerosis. The remaining 50% may be possess the same neoplastic condition in another form.