Autosomal Recessive Sensorineural Hearing Impairment, Dizziness, and Hypodontia

Abstract

• A previously undescribed syndrome with profound sensorineural hearing loss since early infancy, episodes of dizziness, and hypodontia developed in a brother and sister. The presence of two unaffected children and unaffected parents suggests autosomal recessive inheritance. (Arch Otolaryngol 104:292-293, 1978)