Abstract
A Caucasian girl with an unusual dermatosis, similar to cutis marmorata telangiectatica congenita of Van Lohuizen is presented. Four of the 5 main features (congenital phlebectasia, cutis marmorata, superficial ulcerations, and steady improvement) were present. Lacking was spider nevus-like telangiectasias. Recognition is of value as the prognosis is favorable.