Papilledema and Idiopathic Intracranial Hypertension

Abstract

THE development of increased intracranial pressure and papilledema without apparent cause is not uncommon. Since Quincke's¹ original description in 1897, all reported cases have been sporadic and genetically unrelated. The present report is the first to describe this syndrome in two members of the same family. The patients are sisters in whom increased intracranial pressure and papilledema appeared almost simultaneously although they were living over 100 miles apart.Although this condition is well recognized, the terminology has remained an enigma. We propose a new approach to the nomenclature based on the fact that many well known pathologic states aside from . . .