The Glioma-Polyposis Syndrome

Abstract

FAMILIAL polyposis of the colon may be associated with osteomas, fibromas and sebaceous cysts in the Gardner syndrome,¹ with endocrine adenomatosis² and with brain tumors.³ The association with brain tumors was reported by Turcot et al.³ in 1959. To our knowledge the family reported herein (Fig. 1) is the second example of this syndrome.Case ReportCase 1. D.F. (B.M.H. 49262), a 12-year-old girl, was hospitalized on August 8, 1965, 2 weeks after a seizure involving the right arm and leg. She also complained of frontal headache and diarrhea. Her father, who was 47, and her mother, who was 41, . . .