6-Phosphogluconate Dehydrogenase: Hemizygous Manifestation in a Patient with Leukemia

Abstract
In a study of 41 patients with chronic myelocytic leukemia, two were found to have the 6-phosphogluconate dehydrogenase heterozygous phenotype A-B, and two had the phenotype characteristic of PdB homozygosity. Since one of the two with PdB homozygosity was the mother of two children with the A phenotype, it was presumed that she carried a PdA gene not expressed in her blood cells. his was confirmed by electrophoretic analysis of her fibroblasts, which had the A-B phenotypic pattern. Gene deletion is considered to be the most likely explanation.