LENTICONUS ANTERIOR AND ALPORT'S SYNDROME

Abstract

Six patients from 5 families, (5 males and 1 female) suffering from lenticonus anterior are presented. All suffered from chronic nephritis and nerve deafness and must be considered cases of Alport''s syndrome. As all cases with lenticonus anterior which were published within the last 13 yr likewise were affected with nerve deafness and/or chronic nephritis, the lenticonus anterior probably exists exclusively as a part of Alport''s syndrome. Four patients had a weakened bilateral macula reflex with changes in pigmentation. Patients with lenticonus anterior often have a corneal astigmatism of 2-3 diopter. A complete table of all repoted patients with anterior lenticonus is presented.