Elevated lysosomal pH in neuronal ceroid lipofuscinoses (NCLs)
Open Access
- 15 November 2001
- journal article
- research article
- Published by Wiley in European Journal of Biochemistry
- Vol. 268 (22), 5851-5856
- https://doi.org/10.1046/j.0014-2956.2001.02530.x
Abstract
We report here the intracellular (pHi) and lysosomal pH in fibroblasts of six forms of neuronal ceroid lipofuscinoses (NCLs). Acid extrusion rate and pHi values were measured by the membrane‐permeant...Keywords
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