Anomalous origin of left coronary artery from the pulmonary artery with ventricular septal defect.
- 1 May 1978
- journal article
- research article
- Published by Wolters Kluwer Health in Circulation
- Vol. 57 (5), 1026-1030
- https://doi.org/10.1161/01.cir.57.5.1026
Abstract
Only two cases have been reported previously of the association of ventricular septal defect (VSD) with anomalous origin of the left coronary artery (ALCA) arising from the pulmonary artery. The purpose of this paper is to present two additional cases, to describe the pathophysiology, and to emphasize how the clinical course of this combination of defects differs from that of isolated ALCA. Patients with both of these anomalies present in infancy with manifestations only of a large left-right ventricular shunt and pulmonary hypertension. Initially the ALCA is well perfused from the high pressure in the pulmonary artery. In these instances in which the pulmonary artery pressure subsequently decreased because of spontaneous reduction in size of the VSD, the left coronary arterial system became less well perfused. Because of this decreased perfusion in association with the left ventricular myocardial stress initially caused by volume overload, myocardial ischemia and ultimately infarction occurred. Early identification and repair of the anatomic abnormality could prevent irreversible myocardial damage.This publication has 11 references indexed in Scilit:
- Aortic implantation of anomalous left coronary artery arising from pulmonary arteryThe American Journal of Cardiology, 1977
- Subclavian-coronary artery anastomosis in infancy for the Bland-White-Garland syndromeThe Journal of Thoracic and Cardiovascular Surgery, 1976
- Anomalous left coronary arteryThe Journal of Thoracic and Cardiovascular Surgery, 1973
- Anomalous Origin of the Left Coronary Artery from the Right Pulmonary Artery Associated with Ventricular Septal DefectChest, 1970
- Single Coronary Artery, Origin from the Pulmonary Trunk in Association with Ventricular Septal DefectChest, 1970
- Anomalous Origin of the Left Coronary Artery from the Pulmonary TrunkCirculation, 1968
- A method of definitive surgical treatment of anomalous origin of left coronary arteryThe Journal of Thoracic and Cardiovascular Surgery, 1968
- TOTAL CORONARY ARTERIAL CIRCULATION FROM PULMONARY ARTERY WITH SURVIVAL TO AGE 7 - REPORT OF CASE1965
- EditorialCirculation, 1964
- Congenital anomalies of the coronary arteries: Report of an unusual case associated with cardiac hypertrophyAmerican Heart Journal, 1933