Chiari’s Syndrome

Abstract

CHIARI'S syndrome is a rarely observed clinical entity and is seldom diagnosed during life. It was first adequately described by Budd¹ in 1846 but bears the name of Chiari,² who in 1899 reported more completely 3 cases seen in his clinic and collected 7 additional cases. As first described the syndrome was a manifestation of a primary obliterating endophlebitis of the hepatic veins. Other related pathologic processes have subsequently been shown to produce this disease entity.The symptom complex manifested by this syndrome is not generally known. A search of the literature reveals only about 70 reported cases. Out of . . .