SLEEP DISTURBANCE IN PATIENTS WITH JUVENILE NEURONAL CEROID LIPOFUSCINOSIS: A NEW APPLICATION OF THE SCSB-METHOD

Abstract
Five patients (3 male, 2 female, mean age 20.4 yr, range 14-28) with juvenile neuronal ceroid lipofuscinosis (JNCL) were studied using the Static Charge-Sensitive Bed method. Three distinct patterns of respiration (calm, periodic and restless) were differentiated n an automatic analysis. The amount of restless respiration was found to increase with duration of the disease. The result is discussed in terms of methodology and the clinical picture of JNCL.