Infantile Congenital Aneutrocytosis

Abstract

A case of infantile congenital aneutrocytosis is presented. A 2-month-old girl who suffered from infections starting soon after birth, revealed an almost complete absence of neutrophilic myelogenous elements in the peripheral blood and bone marrow. This persisted until she died at the age of 5 months of an overwhelming pulmonary infection. The case seemed to correspond closely with Kostmann''s syndrome, but there was no evidence of genetic background.