A 32 yr old female patient demonstrates the rare combination of a typical IgA nephritis and familial immunothrombocytopenia. Although this association may be purely fortuitous, this observation adds a new facet to a spectrum of reports on (familial) thromborenal syndromes. The pathogenesis of the IgA nephritis has not yet been clarified. Since IgA deposits are found relatively frequently in the mesangium in a number of diverse underlying diseases, there might be common etiological factors. In view of this possibility more attention should be directed to the investigation of IgA associated diseases.