Including the present cases, at least 38 cases of tumors in the nose and throat consisting of brain elements have been described during the last 55 years. They are congenital anomalies which probably represent completely or partially severed remnants of the anterior cerebral vesicle. Our 3 patients illustrate different clinical pictures which may be presented by these tumors. When a tumor is encountered near the nose or in the pharynx, this anomaly should be kept in mind because of the occasional connection with the brain or meninges and the consequent risk of meningitis.