β‐Mannosidase in human leukocytes and fibroblasts
- 3 May 1984
- journal article
- research article
- Published by Wiley in Journal of Inherited Metabolic Disease
- Vol. 7 (4), 155-156
- https://doi.org/10.1007/bf01805598
Abstract
In human leukocytes and fibroblasts β-mannosidase activity has a unimodal pH optimum (4.0–4.5). Markedly reduced activity is found in I-cell disease. Normal activities in human fibroblasts are ten times higher than in the goat, in which species a deficiency disease has been described.This publication has 11 references indexed in Scilit:
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