Renal transport of aromatic acids in patients with phenylketonuria
- 1 December 1981
- journal article
- Published by Wiley in Journal of Inherited Metabolic Disease
- Vol. 4 (1), 69-70
- https://doi.org/10.1007/bf02263595
Abstract
Renal clearance of phenylpyruvic acid is maximal at a plasma concentration of 40–60 µmol/l. This concentration is obtained with plasma phenylalanine concentrations of 1.0–1.2mmol/l, the threshold for separating classical phenylketonuria from phenylketonuria variants.Keywords
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