Short PR intervals and tachyarrhythmias in Fabry's disease
Open Access
- 1 April 1986
- journal article
- case report
- Published by Oxford University Press (OUP)
- Vol. 62 (726), 285-287
- https://doi.org/10.1136/pgmj.62.726.285
Abstract
Summary: Two brothers with Fabry's disease presenting with palpitations were found to have intermittent supraventricular tachycardias. Their electrocardiograms, when symptom-free, revealed short PR intervals consistent with ventricular pre-excitation. Treatment of one of the brothers with verapamil resulted in improvement of the palpitations and reduction in frequency of the tachycardia. Recurrent supraventricular tachycardia associated with ventricular pre-excitation has not previously been described in Fabry's disease. Evidence suggests that this complication may be due to glycolipid deposition in the conducting system around the atrioventricular node.Keywords
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