Congenital Aneurysmal Defect of the Membranous Portion of the Ventricular Septum

Abstract

A case of congenital aneurysmal defect of the ventricular septum is reported which appears to be unique in that this lesion was the only significant finding at autopsy. The patient had evidence of auriculoventricular block for a period of 26 years, at first partial and then complete. She succumbed at the age of 47 to a series of Adams-Stokes attacks which were demonstrated to be set off by paroxysmal ventricular flutter followed by ventricular tachycardia and ventricular standstill. Pertinent literature is briefly reviewed.