Congenital Vascular Veils in the Vitreous

Abstract
Veil-like vascularized sheets of retina extending into the vitreous associated with macular aberration and dendritic retinal atrophy constitute a rare but distinct clinical entity. Restricted to the male sex, this particular intraocular disease is apparently a sex-linked recessive trait. It is the purpose of this presentation to describe the pertinent ocular findings of the afflicted members of two recently discovered families, to give support to the accepted mode of inheritance, to review the scant literature, and to present certain new findings which may possibly extend the scope of this disease. Clinical Characteristics The essential signs which identify "congenital vascular veils in the vitreous" consist of the following: 1. Translucent veil-like membrane (or membranes) projecting into the vitreous, carrying with it the retinal vasculature, which frequently exhibits large ovate dehiscences, and usually present in the inferior temporal quadrant of the globe 2. Perivascular and intraretinal grayish opalescence, suggesting "reactive" or resolution