The clinical and pathologic features of 51 sclerosing hemangiomas of the lung are reviewed. This tumor is benign and occurs predominantly in women. It has a variegated histologic appearance characterized by an admixture of four major histologic patterns: solid, hemorrhagic, papillary, and sclerotic. Characteristic uniform round cells are found within the stroma in all patterns and are unique to this tumor. Sclerosing hemangioma is a distinct clinicopathologic entity and should be distinguished from other benign neoplasms or inflammatory lesions of the lung.