A patient with typical clinical, laboratory and biopsy findings of eosinophilic fasciitis and fulfilling criteria for myositis is reported. Muscular involvement in eosinophilic fasciitis is reviewed and relations to hypereosinophilic syndromes and rheumatoid diseases are discussed. The importance of clinical recognition of eosinophilic fasciitis and histopathological examination of the fascia in the diagnosis of myopathies are underlined.