Normal hydroxylation of proline in collagen synthesized by skin fibroblasts from a patient with prolidase deficiency
- 12 May 1981
- journal article
- research article
- Published by Wiley in Journal of Inherited Metabolic Disease
- Vol. 5 (2), 111-113
- https://doi.org/10.1007/bf01800003
Abstract
The extent of hydroxylation of proline in collagen synthesized and secreted into the culture medium by skin fibroblasts derived from a patient with prolidase deficiency has been examined and found to be normal. It would seem likely that to a considerable extent the urinary proline-containing dipeptides apparent in this condition are derived from sources other than collagen.This publication has 25 references indexed in Scilit:
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