Inflammatory linear verrucous epidermal nevus (ILVEN) in a mother and her daughter

Abstract

Inflammatory linear verrucous epidermal nevus (ILVEN) is a rare skin disease with characteristic clinical and histological changes. The approximately 100 cases so far reported include only one familial occurrence involving a woman and her nephew. We report the occurrence of typical ILVEN in a 47‐year‐old mother and her 17‐year‐old daughter. So far, no clear‐cut genetic interpretation of this observation can be given. Apart from coincidence, various genetic explanations are considered, including X‐linked inheritance with extreme lyonization.