The purpose of this paper is to call attention to a condition which is apparently unfamiliar to most dermatologists. The American dermatologic literature has only one reference to congenital defects.1 This excellent communication of Sutton dealt primarily, however, with a congenital defect of the abdominal walls and only incidentally mentioned congenital defects of the scalp. Our interest in this subject was aroused by a patient presenting a peculiar cicatricial lesion of the scalp. This patient, an infant, was presented before the Los Angeles Dermatological Society on May 11, 1937, at which meeting no one present was able to volunteer a diagnosis. A short time later, Dec. 3, 1937, one of us (F. G. N.2) presented a similar patient before the San Francisco Dermatological Society. At this presentation also no diagnosis was offered. In the meantime one of us had noted an identical condition of the scalp reported in