BULLOUS CONGENITAL ICHTHYOSIFORM ERYTHRODERMA

Abstract
OPINIONS differ as to the nosology of the bullous type of congenital ichthyosiform erythroderma. The pertinent questions that arise regarding this disease are the following: Is it a variant of the nonbullous type? Are the bullae due to a superimposed infection ? How is it clinically and histologically related to other dermatoses of the ichthyosis group? Or, finally, is the infection a combination of ichthyosis and epidermolysis bullosa? In an endeavor to answer these questions we have searched the literature on congenital ichthyosiform erythroderma for examples of the bullous form and have found only 19 such cases reported. Presented here is a history of a typical bullous case which has been under our observation for the past 18 months. A synopsis of the clinical and pathological findings in the 19 cases previously reported is also given. CASES IN THE LITERATURE As first described by Brocq,1 in 1902, congenital ichthyosiform
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