Abnormal auditory evoked potentials in hereditary motor‐sensory neuropathy
- 1 May 1979
- journal article
- research article
- Published by Wiley in Annals of Neurology
- Vol. 5 (5), 445-448
- https://doi.org/10.1002/ana.410050506
Abstract
From a kinship with a dominantly inherited motor-sensory neuropathy, we studied 2 brothers with brainstem auditory evoked potentials and behavioral audiometric tests. They had abnormal prolongation of I-III interpeak intervals. Wave V was poorly developed. Conventional audiometric tests did not reveal a peripheral hearing loss. It is probable that their auditory nerves and spiral ganglia are undergoing a pathophysiological process analogous to that of their peripheral nerves.Keywords
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