A Case of Bronchiolitis Obliterans Organizing Pneumonia Associated with Primary Sjögren’s Syndrome Who Died of Superimposed Diffuse Alveolar Damage

Abstract
Bronchiolitis obliterans organizing pneumonia (BOOP) developed in association with primary Sjögren’s syndrome in a 69-year-old female. She died of diffuse alveolar damage superimposed on BOOP in spite of corticosteroid therapy.