In 1953, Lutz1described a striking arciform eruption of the neck in a young boy and assigned to it the name keratosis follicularis serpiginosa. The biopsy was superficial; the histological studies were sketchy, and the full histopathologic picture was appreciated only in a later review of this case by Miescher.2The disease was reported again in 1955, when Beening and Ruiter3recorded a similar case in a young girl. The next case reported was that of a young boy, seen by Miescher2in 1954 and published the following year. Having the advantage of the histologic specimen from the patient of Lutz, he appreciated that the disease was identical to that described by him but on histologic grounds disagreed with the suggested pathogenicity and proposed the name elastoma intrapapillare perforans verruciforme. In 1956, Gruneberg4reported three cases which he believed