Morquio disease, type B: Activation of GM1-β-galactosidase by GM1-activator protein
- 1 November 1982
- journal article
- research article
- Published by Elsevier in Biochemical and Biophysical Research Communications
- Vol. 109 (2), 568-575
- https://doi.org/10.1016/0006-291x(82)91759-4
Abstract
No abstract availableKeywords
This publication has 14 references indexed in Scilit:
- Aggregation properties of β-galactosidase of human urine and degradation of its natural substrates by a purified preparation of the enzymeBiochimica et Biophysica Acta (BBA) - Protein Structure and Molecular Enzymology, 1982
- β‐galactosidase deficiency: Prolonged survival in three patients following early central nervous system deteriorationClinical Genetics, 1978
- Morquio‐like syndrome with beta galactosidase deficiency and normal hexosamine sulfatase activity: Mucopolysaccharidosis IVBAmerican Journal of Medical Genetics, 1977
- Spondyloepiphyseal dysplasia, corneal clouding, normal intelligence and acid β‐galactosidase deficiencyClinical Genetics, 1976
- Effect of bile salts on lactosylceramide β-galactosidase activities in human brain, liver and cultured skin fibroblastsBiochimica et Biophysica Acta (BBA) - Lipids and Lipid Metabolism, 1975
- G1 Ganglioside β-Galactosidase APublished by Elsevier ,1974
- Ganglioside GM1 β-galactosidase: Studies in human liver and brainArchives of Biochemistry and Biophysics, 1973
- The Purification and Properties of β-Galactosidase from Bovine TestesJournal of Biological Chemistry, 1973
- [121] Corrective factors for inborn errors of mucopolysaccharide metabolismPublished by Elsevier ,1972
- Kolorimetrische mikromethode zur bestimmung des gesamteiweisses in eiweissarmen flüssigkeitenClinica Chimica Acta; International Journal of Clinical Chemistry, 1967