Peritoneal dialysis in maple-syrup-urine disease: Studies on branched-chain amino and keto acids
- 1 June 1980
- journal article
- research article
- Published by Springer Nature in European Journal of Pediatrics
- Vol. 134 (1), 57-63
- https://doi.org/10.1007/bf00442404
Abstract
No abstract availableKeywords
This publication has 14 references indexed in Scilit:
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- INFECTION IN MAPLE-SYRUP-URINE DISEASEThe Lancet, 1971
- PERITONEAL DIALYSIS IN MAPLE SYRUP URINE DISEASEThe Lancet, 1969
- Pathogenesis of maple-syrup-urine disease: observations during dietary management and treatment of coma by peritoneal dialysisBiochemical Medicine, 1969
- Further Observations on the Biochemical Lesion in Maple Syrup Urine DiseaseNature, 1967
- Accelerated chromatography of amino acids associated with phenylketonuria, leucinosis (maple syrup urine disease), and other inborn errors of metabolismAnalytical Biochemistry, 1967
- Studies in Maple Syrup Urine DiseaseArchives of Disease in Childhood, 1961
- Metabolism of the white blood cells in maple-syrup-urine diseaseBiochimica et Biophysica Acta, 1960