The Heart in Dystrophia Myotonica

Abstract

IN a recent review¹ of 85 cases of dystrophia myotonica in which electrocardiographic, roentgenographic or anatomic data, or all, were available it was found that most of the patients manifested changes suggestive or diagnostic of heart disease. Only a few cases were studied post mortem, and in most the description of the heart left much to be desired.^{2 3 4 5 6 7} Recently, we had the opportunity to study a patient with dystrophia myotonica who manifested atrial flutter and died of acute heart failure. The anatomic changes in the heart were striking and form the basis of this report.Case ReportW.D., a 41-year-old . . .