Malignant proliferating pilar tumors arising in KID syndrome: A report of two patients
- 1 March 2007
- journal article
- case report
- Published by Wiley in American Journal of Medical Genetics Part A
- Vol. 143A (7), 734-741
- https://doi.org/10.1002/ajmg.a.31635
Abstract
We report on two young adults with KID syndrome and follicular hyperkeratosis, hidradenitis suppurativa of the groin, progressive development of proliferative pilar cysts and dissecting cellulitis of the scalp, who developed metastatic malignant pilar tumors. Based on our findings, we believe that cancer surveillance in patients with KID syndrome should include screening for pilar tumors and their early removal to avoid development of malignant proliferating pilar tumors with poor prognosis.Keywords
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