Gonadal dysgenesis with 45,X/46,X,dic(Yp) mosaicism

Abstract
A female patient with a gonadal mucinous cystadenoma on the right side and gonadoblastoma on the left was a 45,X/46,X,dic(Yp) mosaic. This brings the total number of cases with dicentric Y chromosome reported to date to 23. The gene on the long arm of the Y chromosome is responsible for the initiation of testicular differentiation, whereas that on the short arm is responsible for the maturation of the testes.