Esthesioneuroblastoma is a rare tumor of nasal-neurogenic origin which because of its close resemblance to the neuroblastomas arising in the adrenal region, is difficult to diagnose. These tumors tend toward local recurrence rather than hematogenous metastases, although the latter occur in advanced cases. The tumor is quite "curable" and our treatment of choice is excisional surgery followed by local radiation therapy to total tumor doses of 5,000 to 6,000 rads in 5 to 6 weeks. The literature is reviewed and 7 additional cases are reported in detail, bringing the total to 104 cases in the world literature.