Successive neuron loss in the thalamus and cortex in a mouse model of infantile neuronal ceroid lipofuscinosis
- 31 January 2007
- journal article
- Published by Elsevier in Neurobiology of Disease
- Vol. 25 (1), 150-162
- https://doi.org/10.1016/j.nbd.2006.09.001
Abstract
No abstract availableKeywords
This publication has 45 references indexed in Scilit:
- Ocular phenotype in a mouse gene knockout model for infantile neuronal ceroid lipofuscinosisJournal of Neuroscience Research, 2006
- Visual deficits in a mouse model of Batten disease are the result of optic nerve degeneration and loss of dorsal lateral geniculate thalamic neuronsNeurobiology of Disease, 2006
- Activation of Non‐neuronal Cells within the Prenatal Developing Brain of Sheep with Neuronal Ceroid LipofuscinosisBrain Pathology, 2006
- CNS-directed AAV2-mediated gene therapy ameliorates functional deficits in a murine model of infantile neuronal ceroid lipofuscinosisMolecular Therapy, 2006
- Thalamocortical neuron loss and localized astrocytosis in the Cln3Δex7/8 knock-in mouse model of Batten diseaseNeurobiology of Disease, 2005
- Progressively reduced synaptic vesicle pool size in cultured neurons derived from neuronal ceroid lipofuscinosis-1 knockout miceNeurobiology of Disease, 2005
- AAV2-mediated ocular gene therapy for infantile neuronal ceroid lipofuscinosisMolecular Therapy, 2005
- Correlations between genotype, ultrastructural morphology and clinical phenotype in the neuronal ceroid lipofuscinosesneurogenetics, 2005
- Hippocampal Pathology in the Human Neuronal Ceroid‐Lipofuscinoses: Distinct Patterns of Storage Deposition, Neurodegeneration and Glial ActivationBrain Pathology, 2004
- Regional and cellular neuropathology in the palmitoyl protein thioesterase-1 null mutant mouse model of infantile neuronal ceroid lipofuscinosisNeurobiology of Disease, 2004