Studies on human N-acetyl-β-d-hexosaminidase C separated from neonatal brain
- 1 April 1976
- journal article
- research article
- Published by Portland Press Ltd. in Biochemical Journal
- Vol. 155 (1), 205-208
- https://doi.org/10.1042/bj1550205
Abstract
Human brain hexosaminidase C (EC 3.2.1.30) was separated from isoenzymes A and B by Sephadex G-200 gel filtration. Properties of the enzyme were studied, particularly its isoelectric-focusing profile, pI 4.80. Hexosaminidase C is identical with the major residual component of Sandhoff fibroblasts with respect to substrate specificity, pI and activity pH optimum.This publication has 20 references indexed in Scilit:
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