Achalasia of the esophagus can result from adenocarcinoma of the stomach or from other tumors that originate in organs adjacent to the esophagus. To the best of our knowledge, we are the first to report achalasia secondary to an hepatic neoplasm. Our patient had typical clinical, radiographic, and manometric features of achalasia with no evidence of direct tumor involvement of the esophagus on barium swallow, computed tomography, angiography, or endoscopy.