Intercurrent illness in inborn errors of intermediary metabolism.
- 1 November 1992
- journal article
- review article
- Published by BMJ in Archives of Disease in Childhood
- Vol. 67 (11), 1387-1391
- https://doi.org/10.1136/adc.67.11.1387
Abstract
Metabolic decompensation may occur in patients with disorders of intermediary metabolism during intercurrent illness. To prevent complications it is normal practice to change the diet to an 'emergency regimen'. The mainstay of this is a high carbohydrate intake, using soluble glucose polymer, given as frequent drinks by day and during the night. Additional therapy is given for some disorders. Practical details of the treatment are outlined.Keywords
This publication has 4 references indexed in Scilit:
- Acute illness in maple syrup urine disease: Dynamics of protein metabolism and implications for managementThe Journal of Pediatrics, 1991
- Renal tubular dysfunction in methylmalonic acidaemiaEuropean Journal of Pediatrics, 1991
- Sources of propionate in inborn errors of propionate metabolismMetabolism, 1990
- Muscle Protein Synthesis Measured by Stable Isotope Techniques in Man: The Effects of Feeding and FastingClinical Science, 1982